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Q82.8 Other specified congenital malformations of skin
BackQ82Other congenital malformations of skinCategory9 →Q82.0Hereditary lymphedemaCategoryQ82.1Xeroderma pigmentosumCategoryQ82.2Congenital cutaneous mastocytosisCategoryQ82.3Incontinentia pigmentiCategoryQ82.4Ectodermal dysplasia (anhidrotic)CategoryQ82.5Congenital non-neoplastic nevusCategoryQ82.6Congenital sacral dimpleCategoryQ82.8Other specified congenital malformations of skinCategoryQ82.9Congenital malformation of skin, unspecifiedCategory
CategoryCODABLE
Q82.8
Other specified congenital malformations of skin
EXAMPLES
Abnormal palmar creases
Accessory skin tags
Benign familial pemphigus [Hailey-Hailey]
Congenital poikiloderma
Cutis laxa (hyperelastica)
Dermatoglyphic anomalies
Inherited keratosis palmaris et plantaris
Keratosis follicularis [Darier-White]
Accessory skin tags
Benign familial pemphigus [Hailey-Hailey]
Congenital poikiloderma
Cutis laxa (hyperelastica)
Dermatoglyphic anomalies
Inherited keratosis palmaris et plantaris
Keratosis follicularis [Darier-White]
EXCLUDES
Excludes1: Ehlers-Danlos syndromes (Q79.6-)
Excludes2: disorders of pyrophosphate metabolism (E83.82-)
Excludes2: disorders of pyrophosphate metabolism (E83.82-)
- Chapter
- XVII · Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
- Section
- Q80-Q89
- Valid from
Source
CMS ICD-10-CM Tabular List, edition FY2026.