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Q82 Other congenital malformations of skin
BackQ82.0Hereditary lymphedemaCategoryQ82.1Xeroderma pigmentosumCategoryQ82.2Congenital cutaneous mastocytosisCategoryQ82.3Incontinentia pigmentiCategoryQ82.4Ectodermal dysplasia (anhidrotic)CategoryQ82.5Congenital non-neoplastic nevusCategoryQ82.6Congenital sacral dimpleCategoryQ82.8Other specified congenital malformations of skinCategoryQ82.9Congenital malformation of skin, unspecifiedCategory
Category
Q82
Other congenital malformations of skin
EXCLUDES
Excludes1: acrodermatitis enteropathica (E83.2)
congenital erythropoietic porphyria (E80.0)
pilonidal cyst or sinus (L05.-)
Sturge-Weber (-Dimitri) syndrome (Q85.89)
congenital erythropoietic porphyria (E80.0)
pilonidal cyst or sinus (L05.-)
Sturge-Weber (-Dimitri) syndrome (Q85.89)
- Chapter
- XVII · Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
- Section
- Q80-Q89
- Valid from
Source
CMS ICD-10-CM Tabular List, edition FY2026.