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Q82.2 Congenital cutaneous mastocytosis
BackQ82Other congenital malformations of skinCategory9 →Q82.0Hereditary lymphedemaCategoryQ82.1Xeroderma pigmentosumCategoryQ82.2Congenital cutaneous mastocytosisCategoryQ82.3Incontinentia pigmentiCategoryQ82.4Ectodermal dysplasia (anhidrotic)CategoryQ82.5Congenital non-neoplastic nevusCategoryQ82.6Congenital sacral dimpleCategoryQ82.8Other specified congenital malformations of skinCategoryQ82.9Congenital malformation of skin, unspecifiedCategory
CategoryCODABLE
Q82.2
Congenital cutaneous mastocytosis
EXAMPLES
Congenital diffuse cutaneous mastocytosis
Congenital maculopapular cutaneous mastocytosis
Congenital urticaria pigmentosa
Congenital maculopapular cutaneous mastocytosis
Congenital urticaria pigmentosa
EXCLUDES
Excludes1: cutaneous mastocytosis NOS (D47.01)
diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
malignant mastocytosis (C96.2-)
systemic mastocytosis (D47.02)
urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)
diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
malignant mastocytosis (C96.2-)
systemic mastocytosis (D47.02)
urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)
- Chapter
- XVII · Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
- Section
- Q80-Q89
- Valid from
Source
CMS ICD-10-CM Tabular List, edition FY2026.