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J84.89 Other specified interstitial pulmonary diseases
BackJ84Other interstitial pulmonary diseasesCategory5 →J84.0Alveolar and parieto-alveolar conditionsCategory4 →J84.01Alveolar proteinosisCategoryJ84.02Pulmonary alveolar microlithiasisCategoryJ84.03Idiopathic pulmonary hemosiderosisCategoryJ84.09Other alveolar and parieto-alveolar conditionsCategoryJ84.1Other interstitial pulmonary diseases with fibrosisCategory3 →J84.10Pulmonary fibrosis, unspecifiedCategoryJ84.11Idiopathic interstitial pneumoniaCategory7 →J84.111Idiopathic interstitial pneumonia, not otherwise specifiedCategoryJ84.112Idiopathic pulmonary fibrosisCategoryJ84.113Idiopathic non-specific interstitial pneumonitisCategoryJ84.114Acute interstitial pneumonitisCategoryJ84.115Respiratory bronchiolitis interstitial lung diseaseCategoryJ84.116Cryptogenic organizing pneumoniaCategoryJ84.117Desquamative interstitial pneumoniaCategoryJ84.17Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhereCategory2 →J84.170Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhereCategoryJ84.178Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhereCategoryJ84.2Lymphoid interstitial pneumoniaCategoryJ84.8Other specified interstitial pulmonary diseasesCategory5 →J84.81LymphangioleiomyomatosisCategoryJ84.82Adult pulmonary Langerhans cell histiocytosisCategoryJ84.83Surfactant mutations of the lungCategoryJ84.84Other interstitial lung diseases of childhoodCategory4 →J84.841Neuroendocrine cell hyperplasia of infancyCategoryJ84.842Pulmonary interstitial glycogenosisCategoryJ84.843Alveolar capillary dysplasia with vein misalignmentCategoryJ84.848Other interstitial lung diseases of childhoodCategoryJ84.89Other specified interstitial pulmonary diseasesCategoryJ84.9Interstitial pulmonary disease, unspecifiedCategory
CategoryCODABLE
J84.89
Other specified interstitial pulmonary diseases
EXAMPLES
Endogenous lipoid pneumonia
Interstitial pneumonitis
Non-specific interstitial pneumonitis NOS
Organizing pneumonia NOS
Interstitial pneumonitis
Non-specific interstitial pneumonitis NOS
Organizing pneumonia NOS
EXCLUDES
Excludes1: cryptogenic organizing pneumonia (J84.116)
idiopathic non-specific interstitial pneumonitis (J84.113)
lipoid pneumonia, exogenous or unspecified (J69.1)
lymphoid interstitial pneumonia (J84.2)
idiopathic non-specific interstitial pneumonitis (J84.113)
lipoid pneumonia, exogenous or unspecified (J69.1)
lymphoid interstitial pneumonia (J84.2)
CODING RULE
Code first: , if applicable:
poisoning due to drug or toxin (T51-T65 with fifth or sixth character to indicate intent), for toxic pneumonopathy
underlying cause of pneumonopathy, if known
Use additional code: code, for adverse effect, to identify drug (T36-T50 with fifth or sixth character 5), if drug-induced
poisoning due to drug or toxin (T51-T65 with fifth or sixth character to indicate intent), for toxic pneumonopathy
underlying cause of pneumonopathy, if known
Use additional code: code, for adverse effect, to identify drug (T36-T50 with fifth or sixth character 5), if drug-induced
- Chapter
- X · Diseases of the respiratory system
- Section
- J80-J84
- Valid from
Source
CMS ICD-10-CM Tabular List, edition FY2026.