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J84.178 Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere

BackJ84Other interstitial pulmonary diseases5 →J84.0Alveolar and parieto-alveolar conditions4 →J84.01Alveolar proteinosisJ84.02Pulmonary alveolar microlithiasisJ84.03Idiopathic pulmonary hemosiderosisJ84.09Other alveolar and parieto-alveolar conditionsJ84.1Other interstitial pulmonary diseases with fibrosis3 →J84.10Pulmonary fibrosis, unspecifiedJ84.11Idiopathic interstitial pneumonia7 →J84.111Idiopathic interstitial pneumonia, not otherwise specifiedJ84.112Idiopathic pulmonary fibrosisJ84.113Idiopathic non-specific interstitial pneumonitisJ84.114Acute interstitial pneumonitisJ84.115Respiratory bronchiolitis interstitial lung diseaseJ84.116Cryptogenic organizing pneumoniaJ84.117Desquamative interstitial pneumoniaJ84.17Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere2 →J84.170Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhereJ84.178Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhereJ84.2Lymphoid interstitial pneumoniaJ84.8Other specified interstitial pulmonary diseases5 →J84.81LymphangioleiomyomatosisJ84.82Adult pulmonary Langerhans cell histiocytosisJ84.83Surfactant mutations of the lungJ84.84Other interstitial lung diseases of childhood4 →J84.841Neuroendocrine cell hyperplasia of infancyJ84.842Pulmonary interstitial glycogenosisJ84.843Alveolar capillary dysplasia with vein misalignmentJ84.848Other interstitial lung diseases of childhoodJ84.89Other specified interstitial pulmonary diseasesJ84.9Interstitial pulmonary disease, unspecified
CategoryCODABLE
J84.178
Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
EXAMPLES
Interstitial pneumonia (nonspecific) (usual) due to collagen vascular disease
Interstitial pneumonia (nonspecific) (usual) in diseases classified elsewhere
Organizing pneumonia due to collagen vascular disease
Organizing pneumonia in diseases classified elsewhere
CODING RULE
Code first: underlying disease, such as:
progressive systemic sclerosis (M34.0)
rheumatoid arthritis (M05.00-M06.9)
systemic lupus erythematosis (M32.0-M32.9)
Chapter
X · Diseases of the respiratory system
Section
J80-J84
Valid from
Source

CMS ICD-10-CM Tabular List, edition FY2026.