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E88.42 MERRF syndrome
BackE88Other and unspecified metabolic disordersCategory8 →E88.0Disorders of plasma-protein metabolism, not elsewhere classifiedCategory3 →E88.01Alpha-1-antitrypsin deficiencyCategoryE88.02Plasminogen deficiencyCategoryE88.09Other disorders of plasma-protein metabolism, not elsewhere classifiedCategoryE88.1Lipodystrophy, not elsewhere classifiedCategory6 →E88.10Lipodystrophy, unspecifiedCategoryE88.11Partial lipodystrophyCategoryE88.12Generalized lipodystrophyCategoryE88.13Localized lipodystrophyCategoryE88.14HIV-associated lipodystrophyCategoryE88.19Other lipodystrophy, not elsewhere classifiedCategoryE88.2Lipomatosis, not elsewhere classifiedCategoryE88.3Tumor lysis syndromeCategoryE88.4Mitochondrial metabolism disordersCategory5 →E88.40Mitochondrial metabolism disorder, unspecifiedCategoryE88.41MELAS syndromeCategoryE88.42MERRF syndromeCategoryE88.43Disorders of mitochondrial tRNA synthetasesCategoryE88.49Other mitochondrial metabolism disordersCategoryE88.8Other specified metabolic disordersCategory3 →E88.81Metabolic syndrome and other insulin resistanceCategory4 →E88.810Metabolic syndromeCategoryE88.811Insulin resistance syndrome, Type ACategoryE88.818Other insulin resistanceCategoryE88.819Insulin resistance, unspecifiedCategoryE88.82Obesity due to disruption of MC4R pathwayCategoryE88.89Other specified metabolic disordersCategoryE88.9Metabolic disorder, unspecifiedCategoryE88.AWasting disease (syndrome) due to underlying conditionCategory
CategoryCODABLE
E88.42
MERRF syndrome
EXAMPLES
Myoclonic epilepsy associated with ragged-red fibers
CODING RULE
Code also: progressive myoclonic epilepsy (G40.3-)
- Chapter
- IV · Endocrine, nutritional and metabolic diseases
- Section
- E70-E88
- Valid from
Source
CMS ICD-10-CM Tabular List, edition FY2026.