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E88.4 Mitochondrial metabolism disorders

BackE88Other and unspecified metabolic disorders8 →E88.0Disorders of plasma-protein metabolism, not elsewhere classified3 →E88.01Alpha-1-antitrypsin deficiencyE88.02Plasminogen deficiencyE88.09Other disorders of plasma-protein metabolism, not elsewhere classifiedE88.1Lipodystrophy, not elsewhere classified6 →E88.10Lipodystrophy, unspecifiedE88.11Partial lipodystrophyE88.12Generalized lipodystrophyE88.13Localized lipodystrophyE88.14HIV-associated lipodystrophyE88.19Other lipodystrophy, not elsewhere classifiedE88.2Lipomatosis, not elsewhere classifiedE88.3Tumor lysis syndromeE88.4Mitochondrial metabolism disorders5 →E88.40Mitochondrial metabolism disorder, unspecifiedE88.41MELAS syndromeE88.42MERRF syndromeE88.43Disorders of mitochondrial tRNA synthetasesE88.49Other mitochondrial metabolism disordersE88.8Other specified metabolic disorders3 →E88.81Metabolic syndrome and other insulin resistance4 →E88.810Metabolic syndromeE88.811Insulin resistance syndrome, Type AE88.818Other insulin resistanceE88.819Insulin resistance, unspecifiedE88.82Obesity due to disruption of MC4R pathwayE88.89Other specified metabolic disordersE88.9Metabolic disorder, unspecifiedE88.AWasting disease (syndrome) due to underlying condition
Category
E88.4
Mitochondrial metabolism disorders
EXCLUDES
Excludes1: disorders of pyruvate metabolism (E74.4)
Kearns-Sayre syndrome (H49.81)
Leber's disease (H47.22)
Leigh's encephalopathy (G31.82)
Mitochondrial myopathy, NEC (G71.3)
Reye's syndrome (G93.7)
Chapter
IV · Endocrine, nutritional and metabolic diseases
Section
E70-E88
Valid from
Source

CMS ICD-10-CM Tabular List, edition FY2026.

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