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D47.02 Systemic mastocytosis
BackD47Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissueCategory7 →D47.0Mast cell neoplasms of uncertain behaviorCategory3 →D47.01Cutaneous mastocytosisCategoryD47.02Systemic mastocytosisCategoryD47.09Other mast cell neoplasms of uncertain behaviorCategoryD47.1Chronic myeloproliferative diseaseCategoryD47.2Monoclonal gammopathyCategoryD47.3Essential (hemorrhagic) thrombocythemiaCategoryD47.4OsteomyelofibrosisCategoryD47.9Neoplasm of uncertain behavior of lymphoid, hematopoietic and related tissue, unspecifiedCategoryD47.ZOther specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissueCategory3 →D47.Z1Post-transplant lymphoproliferative disorder (PTLD)CategoryD47.Z2Castleman diseaseCategoryD47.Z9Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissueCategory
CategoryCODABLE
D47.02
Systemic mastocytosis
EXAMPLES
Indolent systemic mastocytosis
Isolated bone marrow mastocytosis
Smoldering systemic mastocytosis
Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
Isolated bone marrow mastocytosis
Smoldering systemic mastocytosis
Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
EXCLUDES
Excludes1: aggressive systemic mastocytosis (C96.21)
mast cell leukemia (C94.3-)
mast cell leukemia (C94.3-)
CODING RULE
Code also: , if applicable, any associated hematological non-mast cell lineage disease, such as:
acute myeloid leukemia (C92.6-, C92.A-)
chronic myelomonocytic leukemia (C93.1-)
essential thrombocytosis (D47.3)
hypereosinophilic syndrome (D72.1)
myelodysplastic syndrome (D46.9)
myeloproliferative syndrome (D47.1)
non-Hodgkin lymphoma (C82-C85)
plasma cell myeloma (C90.0-)
polycythemia vera (D45)
acute myeloid leukemia (C92.6-, C92.A-)
chronic myelomonocytic leukemia (C93.1-)
essential thrombocytosis (D47.3)
hypereosinophilic syndrome (D72.1)
myelodysplastic syndrome (D46.9)
myeloproliferative syndrome (D47.1)
non-Hodgkin lymphoma (C82-C85)
plasma cell myeloma (C90.0-)
polycythemia vera (D45)
- Chapter
- II · Neoplasms
- Section
- D37-D48
- Valid from
Source
CMS ICD-10-CM Tabular List, edition FY2026.