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D47.01 Cutaneous mastocytosis
BackD47Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissueCategory7 →D47.0Mast cell neoplasms of uncertain behaviorCategory3 →D47.01Cutaneous mastocytosisCategoryD47.02Systemic mastocytosisCategoryD47.09Other mast cell neoplasms of uncertain behaviorCategoryD47.1Chronic myeloproliferative diseaseCategoryD47.2Monoclonal gammopathyCategoryD47.3Essential (hemorrhagic) thrombocythemiaCategoryD47.4OsteomyelofibrosisCategoryD47.9Neoplasm of uncertain behavior of lymphoid, hematopoietic and related tissue, unspecifiedCategoryD47.ZOther specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissueCategory3 →D47.Z1Post-transplant lymphoproliferative disorder (PTLD)CategoryD47.Z2Castleman diseaseCategoryD47.Z9Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissueCategory
CategoryCODABLE
D47.01
Cutaneous mastocytosis
EXAMPLES
Diffuse cutaneous mastocytosis
Maculopapular cutaneous mastocytosis
Solitary mastocytoma
Telangiectasia macularis eruptiva perstans
Urticaria pigmentosa
Maculopapular cutaneous mastocytosis
Solitary mastocytoma
Telangiectasia macularis eruptiva perstans
Urticaria pigmentosa
EXCLUDES
Excludes1: congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
congenital urticaria pigmentosa (Q82.2)
extracutaneous mastocytoma (D47.09)
congenital urticaria pigmentosa (Q82.2)
extracutaneous mastocytoma (D47.09)
- Chapter
- II · Neoplasms
- Section
- D37-D48
- Valid from
Source
CMS ICD-10-CM Tabular List, edition FY2026.