…termination, congenital absence or hypoplasia. Anomalous aortic origin of a coronary artery from the opposite sinus of Valsalva is associated with increased sudden death risk…

…PH in the absence of CTEPH, lung disease, or another explanatory cause. PAH reflects marked pulmonary arterial remodelling, with fibroproliferative, plexogenic, and sometimes thrombotic changes…

…and medical therapies. Adults with congenital heart disease are mostly managed in GUCH clinics (Grown Up Congenital Heart disease). Prevalence of congenital heart disease (CHD…

…anomalous right coronary artery. Anomalous origin of a coronary artery from the pulmonary artery can result in reduced coronary oxygen content, coronary steal, and myocardial…

…the valve (ΔP) from right intraventricular pressure. The systolic PA pressure is an indicator of cardiac hemodynamic status and may be estimated with echocardiography…

…replacement can be performed with biological or mechanical prostheses. The former is preferred due to the lower risk of thrombosis and evidence demonstrating long term…

…quantify the ratio of pulmonary blood flow (Qp) to systemic blood flow (Qs). This measurement is pivotal in diagnosing and managing congenital or acquired cardiac…

…of an X linked condition may develop a phenotype later and require delayed or individualized assessment. Disease specific genetic architecture HCM is predominantly associated with…

…congenital heart disease. Cardiomyopathy leads to impaired cardiac function and heart failure. There are six main types of cardiomyopathy: Hypertrophic cardiomyopathy (HCM) — This type of…

…elastin and is fused with the myocardium. At the departures of the larger vessels, the visceral layer is folded back to cover the inside of…

…often used in combination with meprobamate for the treatment of sleep disorders. <a href="http://www.ncbi.nlm.nih.gov/pubmed/?term=Aceprometazine+AND+(%22QT%22…

…QT dispersion. Increased QT dispersion is associated with increased morbidity and mortality. This is presumably explained by a higher incidence of malignant ventricular arrhythmias. It…

…Complications of atrial fibrillation and available treatments In multivariable models (i.e statistical models in which adjustment has been made for confounders) individuals with atrial…

…gradually causes right ventricular failure. The ventricle and RVOT (right ventricular outflow tract) become dilated, which further agravates the regurgitation. The proximal portion of the…

…visualize clearly with trans thoracic echocardiography. Causes of right ventricular hypertrophy Lung disease (with increased pulmonary vascular resistance), congenital heart disease (transposition of the great…

…disorders , congenital heart disease and catecholamine induced ventricular tachycardia . The vast majority of patients with ventricular tachycardia either have coronary artery disease (ischemic heart disease)…

…due to sinus pause or post VPC pause) results in augmentation of early afterdpolarization amplitude (typically seen with large T wave amplitude), and QT prolongation…

…A, Lange Nielsen F. Congenital deaf mutism, functional heart disease with prolongation of the Q T interval and sudden death. Am Heart J 1957;54…

…and young adults with congenital heart disease. Initiation Strategies Because of its ability to significantly prolong the QT interval and cause torsades de pointes or…

…due to sinus pause or post VPC pause) results in augmentation of early afterdpolarization amplitude (typically seen with large T wave amplitude), and QT prolongation…

…prolapse of P2 (Figure 1). Myocardial ischemia affecting the papillary muscles or the connected myocardium may cause mitral prolapse, and thus regurgitation. Ischemia manifests with…

…the right ventricle and right atrium, leading to right heart hypertrophy, dilation and ultimately right heart failure. Echocardiography in mitral stenosis Echocardiographic assessment of mitral…