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Q33.0 Congenital cystic lung
BackQ33Congenital malformations of lungCategory9 →Q33.0Congenital cystic lungCategoryQ33.1Accessory lobe of lungCategoryQ33.2Sequestration of lungCategoryQ33.3Agenesis of lungCategoryQ33.4Congenital bronchiectasisCategoryQ33.5Ectopic tissue in lungCategoryQ33.6Congenital hypoplasia and dysplasia of lungCategoryQ33.8Other congenital malformations of lungCategoryQ33.9Congenital malformation of lung, unspecifiedCategory
CategoryCODABLE
Q33.0
Congenital cystic lung
EXAMPLES
Congenital cystic lung disease
Congenital honeycomb lung
Congenital polycystic lung disease
Congenital honeycomb lung
Congenital polycystic lung disease
EXCLUDES
Excludes1: cystic fibrosis (E84.0)
cystic lung disease, acquired or unspecified (J98.4)
cystic lung disease, acquired or unspecified (J98.4)
- Chapter
- XVII · Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
- Section
- Q30-Q34
- Valid from
Source
CMS ICD-10-CM Tabular List, edition FY2026.