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I27.83 Eisenmenger's syndrome

CategoryCODABLE
I27.83
Eisenmenger's syndrome
EXAMPLES
Eisenmenger's complex
(Irreversible) Eisenmenger's disease
Pulmonary hypertension with right to left shunt related to congenital heart disease
CODING RULE
Code also: underlying heart defect, if known, such as:
atrial septal defect (Q21.1-)
Eisenmenger's defect (Q21.8)
patent ductus arteriosus (Q25.0)
ventricular septal defect (Q21.0)
Chapter
IX · Diseases of the circulatory system
Section
I26-I28
Valid from
Source

CMS ICD-10-CM Tabular List, edition FY2026.