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E84.0 Cystic fibrosis with pulmonary manifestations

CategoryCODABLE
E84.0
Cystic fibrosis with pulmonary manifestations
CODING RULE
Use additional code: code to identify any infectious organism present, such as:
Pseudomonas (B96.5)
Chapter
IV · Endocrine, nutritional and metabolic diseases
Section
E70-E88
Valid from
Source

CMS ICD-10-CM Tabular List, edition FY2026.