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E77.0 Defects in post-translational modification of lysosomal enzymes

CategoryCODABLE
E77.0
Defects in post-translational modification of lysosomal enzymes
EXAMPLES
Mucolipidosis II [I-cell disease]
Mucolipidosis III [pseudo-Hurler polydystrophy]
Chapter
IV · Endocrine, nutritional and metabolic diseases
Section
E70-E88
Valid from
Source

CMS ICD-10-CM Tabular List, edition FY2026.