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ICD-10-CM/Endocrine, nutritional and metabolic diseases/Metabolic disorders/Disorders of glycosaminoglycan metabolism

E76.0 Mucopolysaccharidosis, type I

BackE76Disorders of glycosaminoglycan metabolismCategory6 →E76.0Mucopolysaccharidosis, type ICategory3 →E76.01Hurler's syndromeCategoryE76.02Hurler-Scheie syndromeCategoryE76.03Scheie's syndromeCategoryE76.1Mucopolysaccharidosis, type IICategoryE76.2Other mucopolysaccharidosesCategory3 →E76.21Morquio mucopolysaccharidosesCategory3 →E76.210Morquio A mucopolysaccharidosesCategoryE76.211Morquio B mucopolysaccharidosesCategoryE76.219Morquio mucopolysaccharidoses, unspecifiedCategoryE76.22Sanfilippo mucopolysaccharidosesCategoryE76.29Other mucopolysaccharidosesCategoryE76.3Mucopolysaccharidosis, unspecifiedCategoryE76.8Other disorders of glucosaminoglycan metabolismCategoryE76.9Glucosaminoglycan metabolism disorder, unspecifiedCategory
Category
E76.0
Mucopolysaccharidosis, type I
Chapter
IV · Endocrine, nutritional and metabolic diseases
Section
E70-E88
Valid from
Source

CMS ICD-10-CM Tabular List, edition FY2026.

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