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E74.09 Other glycogen storage disease

BackE74Other disorders of carbohydrate metabolism7 →E74.0Glycogen storage disease7 →E74.00Glycogen storage disease, unspecifiedE74.01von Gierke diseaseE74.02Pompe diseaseE74.03Cori diseaseE74.04McArdle diseaseE74.05Lysosome-associated membrane protein 2 [LAMP2] deficiencyE74.09Other glycogen storage diseaseE74.1Disorders of fructose metabolism4 →E74.10Disorder of fructose metabolism, unspecifiedE74.11Essential fructosuriaE74.12Hereditary fructose intoleranceE74.19Other disorders of fructose metabolismE74.2Disorders of galactose metabolism3 →E74.20Disorders of galactose metabolism, unspecifiedE74.21GalactosemiaE74.29Other disorders of galactose metabolismE74.3Other disorders of intestinal carbohydrate absorption2 →E74.31Sucrase-isomaltase deficiencyE74.39Other disorders of intestinal carbohydrate absorptionE74.4Disorders of pyruvate metabolism and gluconeogenesisE74.8Other specified disorders of carbohydrate metabolism3 →E74.81Disorders of glucose transport, not elsewhere classified3 →E74.810Glucose transporter protein type 1 deficiencyE74.818Other disorders of glucose transportE74.819Disorders of glucose transport, unspecifiedE74.82Disorders of citrate metabolism2 →E74.820SLC13A5 Citrate Transporter DisorderE74.829Other disorders of citrate metabolismE74.89Other specified disorders of carbohydrate metabolismE74.9Disorder of carbohydrate metabolism, unspecified
CategoryCODABLE
E74.09
Other glycogen storage disease
EXAMPLES
Andersen disease
Glycogen storage disease, types 0, IV, VI-XI
Hers disease
Liver phosphorylase deficiency
Muscle phosphofructokinase deficiency
Tauri disease
Chapter
IV · Endocrine, nutritional and metabolic diseases
Section
E70-E88
Valid from
Source

CMS ICD-10-CM Tabular List, edition FY2026.