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D75.81 Myelofibrosis
BackD75Other and unspecified diseases of blood and blood-forming organsCategory5 →D75.0Familial erythrocytosisCategoryD75.1Secondary polycythemiaCategoryD75.8Other specified diseases of blood and blood-forming organsCategory5 →D75.81MyelofibrosisCategoryD75.82Heparin induced thrombocytopenia (HIT)Category4 →D75.821Non-immune heparin-induced thrombocytopeniaCategoryD75.822Immune-mediated heparin-induced thrombocytopeniaCategoryD75.828Other heparin-induced thrombocytopenia syndromeCategoryD75.829Heparin-induced thrombocytopenia, unspecifiedCategoryD75.83ThrombocytosisCategory2 →D75.838Other thrombocytosisCategoryD75.839Thrombocytosis, unspecifiedCategoryD75.84Other platelet-activating anti-PF4 disordersCategoryD75.89Other specified diseases of blood and blood-forming organsCategoryD75.9Disease of blood and blood-forming organs, unspecifiedCategoryD75.AGlucose-6-phosphate dehydrogenase (G6PD) deficiency without anemiaCategory
CategoryCODABLE
D75.81
Myelofibrosis
EXAMPLES
Myelofibrosis NOS
Secondary myelofibrosis NOS
Secondary myelofibrosis NOS
EXCLUDES
Excludes1: acute myelofibrosis (C94.4-)
idiopathic myelofibrosis (D47.1)
leukoerythroblastic anemia (D61.82)
myelofibrosis with myeloid metaplasia (D47.4)
myelophthisic anemia (D61.82)
myelophthisis (D61.82)
primary myelofibrosis (D47.1)
idiopathic myelofibrosis (D47.1)
leukoerythroblastic anemia (D61.82)
myelofibrosis with myeloid metaplasia (D47.4)
myelophthisic anemia (D61.82)
myelophthisis (D61.82)
primary myelofibrosis (D47.1)
CODING RULE
Code first: the underlying disorder, such as:
malignant neoplasm of breast (C50.-)
Use additional code: code, if applicable, for associated therapy-related myelodysplastic syndrome (D46.-)
code for adverse effect, if applicable, to identify drug (T45.1X5)
malignant neoplasm of breast (C50.-)
Use additional code: code, if applicable, for associated therapy-related myelodysplastic syndrome (D46.-)
code for adverse effect, if applicable, to identify drug (T45.1X5)
- Chapter
- III · Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
- Section
- D70-D77
- Valid from
Source
CMS ICD-10-CM Tabular List, edition FY2026.