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D56.0 Alpha thalassemia
BackD56ThalassemiaCategory8 →D56.0Alpha thalassemiaCategoryD56.1Beta thalassemiaCategoryD56.2Delta-beta thalassemiaCategoryD56.3Thalassemia minorCategoryD56.4Hereditary persistence of fetal hemoglobin [HPFH]CategoryD56.5Hemoglobin E-beta thalassemiaCategoryD56.8Other thalassemiasCategoryD56.9Thalassemia, unspecifiedCategory
CategoryCODABLE
D56.0
Alpha thalassemia
EXAMPLES
Alpha thalassemia major
Hemoglobin H Constant Spring
Hemoglobin H disease
Hydrops fetalis due to alpha thalassemia
Severe alpha thalassemia
Triple gene defect alpha thalassemia
Hemoglobin H Constant Spring
Hemoglobin H disease
Hydrops fetalis due to alpha thalassemia
Severe alpha thalassemia
Triple gene defect alpha thalassemia
EXCLUDES
Excludes1: alpha thalassemia trait or minor (D56.3)
asymptomatic alpha thalassemia (D56.3)
hydrops fetalis due to isoimmunization (P56.0)
hydrops fetalis not due to immune hemolysis (P83.2)
asymptomatic alpha thalassemia (D56.3)
hydrops fetalis due to isoimmunization (P56.0)
hydrops fetalis not due to immune hemolysis (P83.2)
CODING RULE
Use additional code: code, if applicable, for hydrops fetalis due to alpha thalassemia (P56.99)
- Chapter
- III · Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
- Section
- D55-D59
- Valid from
Source
CMS ICD-10-CM Tabular List, edition FY2026.