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Q56 Indeterminate sex and pseudohermaphroditism
BackQ56.0Hermaphroditism, not elsewhere classifiedCategoryQ56.1Male pseudohermaphroditism, not elsewhere classifiedCategoryQ56.2Female pseudohermaphroditism, not elsewhere classifiedCategoryQ56.3Pseudohermaphroditism, unspecifiedCategoryQ56.4Indeterminate sex, unspecifiedCategory
Category
Q56
Indeterminate sex and pseudohermaphroditism
EXCLUDES
Excludes1: 46,XX true hermaphrodite (Q99.1)
androgen insensitivity syndrome (E34.5-)
chimera 46,XX/46,XY true hermaphrodite (Q99.0)
female pseudohermaphroditism with adrenocortical disorder (E25.-)
pseudohermaphroditism with specified chromosomal anomaly (Q96-Q99)
pure gonadal dysgenesis (Q99.1)
androgen insensitivity syndrome (E34.5-)
chimera 46,XX/46,XY true hermaphrodite (Q99.0)
female pseudohermaphroditism with adrenocortical disorder (E25.-)
pseudohermaphroditism with specified chromosomal anomaly (Q96-Q99)
pure gonadal dysgenesis (Q99.1)
- Chapter
- XVII · Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
- Section
- Q50-Q56
- Valid from
Source
CMS ICD-10-CM Tabular List, edition FY2026.