ICD-10 Code: E76.0 – Mucopolysaccharidosis, type I
ICD-10 code E76.0 corresponds to Mucopolysaccharidosis, type I. This code is classified under the chapter E76 Disorders of glycosaminoglycan metabolism, which is part of the E70-E88: Metabolic disorders category.
The parent chapter is Endocrine, nutritional and metabolic diseases.